The following is a list of hereditary metabolic defectsinvolving loss of single enzymes of catabolism, and a second listof possible consequences of such defects. Match each enzyme withits most likely consequence (only one).
A. lack of phosphoglucomutase
B. lack of UDP-glucose pyrophosphorylase
C. lack of triose phosphate isomerase
D. lack of phosphofructokinase
E. lack of glycogen phosphorylase kinase
F. lack of ?-1,6-glucosidase
1. impaired ability to obtain energy from carbohydrates.
2. lower than normal production of glucose 1-P fromglycogenolysis.
3. inability to use either glycogen or galactose as an energysource
4. inability to use galactose as an energy source, with noeffect on ability to use glycogen.
5. lethal; prevents use of carbohydrates for ATP production
6. inability to use glycogen as an energy source, with no effecton ability to use galactose.
The following is a list of hereditary metabolic defectsinvolving loss of single enzymes of catabolism, and a second listof possible consequences of such defects. Match each enzyme withits most likely consequence (only one).
A. | lack of phosphoglucomutase | |||||||||||
B. | lack of UDP-glucose pyrophosphorylase | |||||||||||
C. | lack of triose phosphate isomerase | |||||||||||
D. | lack of phosphofructokinase | |||||||||||
E. | lack of glycogen phosphorylase kinase | |||||||||||
F. lack of ?-1,6-glucosidase
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